DIAGNOSIS AND TREATMENT COMBINED DEFICIENCY OF BLOOD COAGULATION FACTORS V AND VIII IN THE REPUBLIC OF UZBEKISTAN
Ключевые слова:
Rare bleeding disorders, combined deficiency of FV FVIII, hematoma, cephalohematoma, hemarthrosis.Аннотация
Hereditary rare coagulopathies are a heterogeneous group of qualitative or quantitative factor deficiencies, including deficiencies of fibrinogen, factors II, V, VII, VIII, IX, X, XI, XIII, von Willebrand factor, combined deficiency of FV+FVIII and hereditary combined deficiency of vitamin K- dependent coagulation factors. Congenital bleeding disorders are typically diagnosed in patients at birth, trauma, surgery, and other situations involving blood loss. The clinical manifestations of these diseases significantly reduce the quality of life of patients and can often be life-threatening and develop complications that can lead to early disability of patients [5,6].
Библиографические ссылки
Juraeva N. T., Mahmudova A. D.,Madashova A.G. Hereditary deficiency of blood coagulation factor X, clinical observations. medical center of hematology of the ministry of health of the republic of uzbekistan.Internet address: http://ifsrp.edu.ge/ E-mail: info@ifsrp.edu.ge/ Published by Institute for Scientific Research and Publication & Research and Publishing Center virtualconferences.press Issued monthly DOI prefix: 10.5281/zenodo.5889885 Hausarztzentrum Aachen-ForstTrierer Str. 67, 52078 Aachener, Germany
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