DIAGNOSIS AND TREATMENT COMBINED DEFICIENCY OF BLOOD COAGULATION FACTORS V AND VIII IN THE REPUBLIC OF UZBEKISTAN
Keywords:
Rare bleeding disorders, combined deficiency of FV FVIII, hematoma, cephalohematoma, hemarthrosis.Abstract
Hereditary rare coagulopathies are a heterogeneous group of qualitative or quantitative factor deficiencies, including deficiencies of fibrinogen, factors II, V, VII, VIII, IX, X, XI, XIII, von Willebrand factor, combined deficiency of FV+FVIII and hereditary combined deficiency of vitamin K- dependent coagulation factors. Congenital bleeding disorders are typically diagnosed in patients at birth, trauma, surgery, and other situations involving blood loss. The clinical manifestations of these diseases significantly reduce the quality of life of patients and can often be life-threatening and develop complications that can lead to early disability of patients [5,6].
References
Juraeva N. T., Mahmudova A. D.,Madashova A.G. Hereditary deficiency of blood coagulation factor X, clinical observations. medical center of hematology of the ministry of health of the republic of uzbekistan.Internet address: http://ifsrp.edu.ge/ E-mail: info@ifsrp.edu.ge/ Published by Institute for Scientific Research and Publication & Research and Publishing Center virtualconferences.press Issued monthly DOI prefix: 10.5281/zenodo.5889885 Hausarztzentrum Aachen-ForstTrierer Str. 67, 52078 Aachener, Germany
Juraeva N. T., Makhmudova A.D, Ismoilova Z.A, Hereditary deficiency of blood coagulation factor V- hypoproaccelerinemia, clinical observations, France, Scientific Approach to the modern education system. Part 6, 31july, 2022, www.interonconf.com p-262-268.
Juraeva N. T., Makhmudova A.D, Ismoilova Z.A, Hereditary deficiency of blood coagulation factor I - afibrinogenemia, clinical observation. Texas Journal of multidisciplinary studies, https://zienjournals.com/ISSN N0:2770-2936, 30-07-2022:
Juraeva N. T., Makhmudova A.D, Radjabova M.O, Ismoilova Z.A, Incidence and laboratory features of rare coagulopathy in patients in the Republic of Uzbekistan, Dehli, India-2022, International online, scientific art journal Young Academik ISBN:9789393695505/ volume 4, August 2022/ pp17-21.
Juraeva N. T., Makhmudova A.D, Davlatova G.N., Ismoilova Z.A, «Treatment and incidence of von Willebrand's disease in the Republic of Uzbekistan» Texas Journal of medical science https://zienjournals.com/index.php/tjms/article/view/2196
Juraeva N. T., Makhmudova, A.D, Madashova A.G. Deficiency Of Blood Coagulation Factor VII – Hypoproconvertinamia «Journal of Community PharmacyPractice”,http://journal.hmjournals.com/index.php/JCPP/article/view/403
Juraeva N. T., Frequency of occurrence and laboratory features of rare coagulopathies. Journal of Prevention, Diagnosis and Management of Human Diseases, ISSN:2799-1202: Vol:02,№01, Dec 2021-Jan 2022;1-5.
Juraeva N. T.,Mahmudova A. D.,Radjabova M.O. Hereditary coagulation factor II deficiency – Hypothrombinemia,Copyright © 2022 By Primedia E-launch LLC All rights reserved. Available at virtualconferences.press Published Primedia E-launch LLC. Shawnee, USA ISBN 978-1-64945-234-4 DOI:10.5281/zenodo.5091677 Primedia E-launch LLC, 5518 Flint St, Shawnee, 66203,USA,https://orcid.org/0000-00019154-6049 instituteforscientificresearch@gmail.com.
Kobayashi T, Kanayama N. Prenatal and peripartum management of congenital afibrinogaenemia. Br J Haematol 2009;109:364-6. Karimi M, Menegatti M, Afrasiabi A, et al. Phenotype and genotype report on homozygous and heterozygous patients with congenital factor X deficiency. Haematologica 2009;93:934-8.
Kadir R, Chi C, Bolton-Maggs P. Pregnancy and rare bleeding disorders. Haemophilia 2009;15:990-1005.
Kobayashi T, Nakabayashi M, Yoshioka A et al. Recombinant activated factor VII (rFVIIa/ NovoSeven®) in the management of severe postpartum haemorrhage: initial report of a multicentre case series in Japan. Int J Hematol., 2012, 5(1): 57-63.
